Defects of Secretion in Cystic Fibrosis - Advances in Experimental Medicine and Biology 2005 edition

Marc Notes: Includes bibliographical references and index. Table of Contents: Contributing Authors.- Preface.- Acknowledgments.- Outside Neurons/Inside Epithelia: Novel Activation of CFTR Cl- and HCO3-Conductances.- Role of CFTR and other Ion Channels In Cystic Fibrosis.- Ion Channels in the Apical mEmbrane: Role of Electrical Coupling on Transepithelial Transport.- Ion channels in secretory granules of the pancreas: Molecular identification and their role in regulated secretion.- Epithelial Transport and Intracellular Trafficking: Physiology and Pathophysiology.- Kinases, Cell Volume, and the Regulation of Chloride Channels.- The CLCAs: Proteins with Ion Channel, Cell Adhesion and Tumor Suppressor Functions.- Is Intervention in Inositol Phosphate Signaling a Useful Therapeutic Option for Cystic Fibrosis?- An Inositol Phosphate Analog, INO-4995, Normalizes Electrophysiology in CF Airway Epithelia.- Vitamin C and Flavonoids Potentiate CFTR Cl Transport in Human Airway Epithelia.- Airway Glycoconjugates Secreted in Cystic Fibrosis and Severe Chronic Airway Inflammation Relationship with Pseudomonas aeruginosa.- Biosynthesis and Secretion of Mucins, Especially the MUC2 MUCIN, in Relation to Cystic Fibrosis.- Index.